Wunderlich’s Syndrome – Spontaneous Rupture of a Giant Renal Angiomyolipoma
Keywords:
Giant angiomyolipoma (AML) of kidney, Wunderlich’s syndrome, Hypovolemic shock, Retroperitoneal haemorrhage, NephrectomyAbstract
This is a rare case of spontaneous rupture of a giant renal angiomyolipoma (AML), with symptoms of hypovolemic shock (Wunderlich’s syndrome), which was managed by total nephrectomy. Enlarged renal AMLs can rupture. This can be sudden and painful with manifestations of hypovolemic shock. The management of AMLs has been correlated with symptoms. Patients with life threatening retroperitoneal haemorrhage, require exploration as retroperitoneal bleeding can lead to severe complications, increasing morbidity. In case of giant angiomyolipoma with intratumoral haemorrhage, and symptoms of Wunderlich’s syndrome, partial or total nephrectomy is a good treatment option.
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