A Rare Case of Bleeding Disorder: Glanzmann’s Thrombasthenia
DOI:
https://doi.org/10.46858/vimshsj.8306Keywords:
Platelet, Bleeding, Hemorrhage, EpistaxisAbstract
Glanzmann’s thrombasthenia is an extremely rare autosomal recessive inherited bleeding disorder characterized by defective platelet aggregation leading to prolonged bleeding time. Patients may present with easy bruising, purpura, epistaxis, menorrhagia and gingival bleeding. Though the disease is rare, the prognosis is usually excellent with supportive care. Here, we report the case of Glanzmann’s thrombasthenia in a young female who presented with complaints of epistaxis and a history of easy bruising. The patient improved with symptomatic and supportive care. The patient got discharged and is doing well under regular follow-up.
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Copyright (c) 2021 Dr. Karthik Kolkur, Dr. Sanjay Chavan, Dr. Darshita Shukla, Dr. Sharad Agarkhedkar
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