Pierre Robin Syndrome: A Case Report
Keywords:
Cleft palate, Micrognathia, Glossoptosis, Pierre Robin syndromeAbstract
Pierre Robin syndrome a well-recognized congenital condition characterized by micrognathia, glossoptosis and palatal malformation. Pierre Robin syndrome is also called pierre Sequence because it is caused by sequence of events that happen in the womb, which affects the way the baby develops. We report a case of a one day neonate who presented with complaints of feeding and respiratory difficulty and was later diagnosed as case of Pierre Robin syndrome. The primary defect lies in the arrested development of mandible leading to a characteristic bird face appearance.
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